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Issue Date
2015-05-21Keywords
Enfermedad de Gorham-StoutOsteólisis esencial;
Linfangioma
Lymphangioma
Gorham-Stout disease
Essential osteolysis
Metadata
Show full item recordOther Titles
Atypical presentation of Gorham-Stout syndrome. Case reportPublisher
Sociedad Argentina de PediatríaJournal
Archivos argentinos de pediatría (Arch. argent. pediatr.)DOI
10.5546/aap.2015.e153Additional Links
http://www.scielo.org.ar/scielo.php?pid=S0325-00752015000300017&script=sci_arttext&tlng=esAbstract
El síndrome de Gorham-Stout es una patología ósea extremadamente rara de etiología desconocida, caracterizada histopatológicamente por proliferación de los canales vasculares, que origina destrucción y resorción de la matriz ósea. Se presenta el caso de un paciente varón de nueve años de edad con un cuadro agudo caracterizado por fiebre, dolor torácico, dificultad respiratoria y disnea ante pequeños esfuerzos. Se realizaron estudios de imágenes y patología, en los que se encontraron lesiones liticas múltiples y presencia de un linfangioma mediastínico. Se diagnosticó síndrome de Gorham-Stout. Esta es una presentación atípica debido a la localización de la linfangiomatosis y al tamaño de la masa.Type
info:eu-repo/semantics/articleRights
info:eu-repo/semantics/openAccessLanguage
spaDescription
Gorham-Stout syndrome is an extremely rare pathology, of unknown etiology. It is characterized by proliferation of vascular channels that causes destruction and reabsorption of the bone matrix. We present a nine year-old male patient with an acute episode characterized by fever, chest pain, respiratory distress and dyspnea. The patient was submitted to computed tomography scan and a biopsy. The findings in the biopsy were multiple lytic lesions, osteolysis, and a mediastinal lymphangioma (lymphangiomatosis). The diagnosis was Gorham-Stout syndrome with atypical presentation.[email protected]
ISSN
0325-0075ae974a485f413a2113503eed53cd6c53
10.5546/aap.2015.e153
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